verezdoВестник репродуктивного здоровьяBulletin of Reproductive Health2075-65692310-421XEndocrinology Research Centre (Moscow)10.14341/brh20083-448-51verezdo-8541Research ArticleСтатьиArticlesНовая классификация заболеваний, связанных с нарушением формирования пола. Обсуждение международного консенсуса по пересмотру терминологии и классификации гермафродитизмаNovaya klassifikatsiya zabolevaniy, svyazannykh s narusheniem formirovaniya pola. Obsuzhdenie mezhdunarodnogo konsensusa po peresmotru terminologii i klassifikatsii germafroditizmaКалинченкоН ЮKalinchenkoN Yu-ТюльпаковА НTyul'pakovA N-ФГУ Эндокринологический научный центр Росмедтехнологий20081512200803-4№3-4 (2008)4851Copyright © Калинченко Н.Ю., Тюльпаков А.Н., 20082008Калинченко Н.Ю., Тюльпаков А.Н.Kalinchenko N.Y., Tyul'pakov A.N.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.vrz-endojournals.ru/jour/article/view/8541

Нарушение формирования пола — состояние, связанное с клинико-биохимическим проявлением несоответствия между генетическим, гонадным и фенотипическим полом ребенка. Традиционно для описания данного состояния используется термин«гермафродитизм».В биологии под гермафродитизмом понимают одновременное или последовательное наличие мужских и женских половых признаков и репродуктивных органов у раздельнополых организмов. Различают естественный гермафродитизм, присущий различным видам животных и растений, и аномальный (патологический) гермафродитизм, встречающийся у раздельнополых животных. Термин «гермафродитизм» произошел от слияния имен двух греческих богов — Гермес (Hermes, бог мужской силы и сексуальности — составной части его божественных качеств) и Афродита (Afrodite, богиня женской красоты, любви и сексуальности). Так как при рождении ребенка с неправильным строением наружных половых органов половую принадлежность без дополнительных исследований определить сложно, этот термин также стали применять для описания данного клинического состояния в медицине, подчеркивая неопределенность, двойственность пола. При классификации гермафродитизма ориентировались на кариотип пациента: при кариотипе 46хх состояние расценивалось как женский гермафродитизм, при кариотипе 46хУ — как мужской гермафродитизм, при обнаружении гонад обоего пола у одного пациента — как истинный гермафродитизм. Однако в последнее время данная классификация перестала удовлетворять как пациентов, так и врачей.

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The authors declare that there are no conflicts of interest present.